How is refractory thrombotic thrombocytopenic purpura (TTP) treated?
Options include increased frequency of plasma exchange, rituximab, and immunosuppressive therapies such as cyclophosphamide and vincristine.
Options include increased frequency of plasma exchange, rituximab, and immunosuppressive therapies such as cyclophosphamide and vincristine.
Cardiac troponin, BUN and creatine, urinalysis, electrocardiogram and CT brain if neurological symptoms.
ADAMTS13 activity level
70%-80% of cases
10-30 × 109/L
8-10 g/dL
5% of patients