How is hemophagocytic lymphohistiocytosis (HLH) treated?
The patient is started on dexamethasone with rapid improvement in his clinical symptoms as well as laboratory indices. He is discharged with plan for a prolonged corticosteroid taper.
At outpatient follow-up 1 month after discharge, he reports no recurrence of his presenting symptoms. Outpatient lab work demonstrates complete normalization of his inflammatory works and cytopenias.
His final diagnosis is acquired hemophagocytic lymphohistiocytosis due to probable undefined infection.
What is the overall mortality of secondary hemophagocytic lymphohistiocytosis (HLH)?