Knowledge check

True of false: Acute chest syndrome rarely occurs in HbSC disease. It is almost exclusively a condition associated with HbSS.

a

True

b

False

True of false: Acute chest syndrome may be more severe in patients with HbSC compared to HbSS because baseline hemoglobin tends to higher in HbSC.

a

True

b

False

What are the 2 diagnostic criteria for acute chest syndrome (ACS)?

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Respiratory symptoms
New infiltrate on CXR

Which of the following are treatment recommendations in all patients with acute chest syndrome (ACS)?

a

Exchange transfusion

Only in the more severe cases or in those with high baseline hemoglobin.

b

Antibiotics

c

Incentive spirometry

d

Therapeutic anticoagulation